Epithelioid Hemangioendothelioma (EH) is a
rare malignant vascular tumour that is considered to be
intermediate grade between benign Hemangioma and
malignant Angiosarcoma originates from vascular
endothelial or Pre endothelial cells. EH can occur
anywhere in the body most commonly affects the Liver,
Lungs, Bones, and although involves the Pleura,
Mediastinum, Spleen, Skin, Breast, Head and neck area,
Brain and Meninges and Lymph nodes. It often involves
either superficial or deep soft tissue, visceral organs and
less commonly, medium-size or large veins. The aetiology
is unknown and is usually diagnosed at young adult,
being rare in children. EH is locally aggressive,
heterogenous and represents less than 1% of all the
vascular tumours and capable of metastasis. Prevalence
is 1 in 1 million.
A 45Years old male presented with soft to firm
subcutaneous swelling since 7years later it progressed
rapidly in size from 1year in the Right upper anterior
chest. On examination: A non-tender, multilobulated
exophytic lesion in the subcutaneous plane showing few
erythematous nodules of varying size and were firm in
consistency. High frequency Ultrasound.(US) of Right
Supraclavicular Mass, and MRI Thorax modalities
suggest features of Supraclavicular soft tissue neoplasm
showing vascular components and concern for
Hemangioendothelioma.
Management includes wide excision of the soft
tissue lesion in the supraclavicular region and followed
by excisional biopsy and histopathological confirmation.
US and most sensitiveMagnetic Resonance
Imaging(MRI) modality features along with
pathological techniques of Histopathology and
Immunohistochemistry(IHC) techniques confirms the
vascular nature of tumour. Followed by the wide excision
the patient has undergone adjuvant radiation therapy to
decrease the risk of local recurrence and distant
metastasis
Keywords : CT Computed Tomography, Epithelioid Hemangioendothelioma, Immunohistochemistry, Magnetic Resonance Imaging, Out Patient Department, T1 Weighted Images, T2 Weighted Images, Ultrasound.